Paraganglioma of the Thyroid Gland

Paragangliomas (PGs) are rare neuroendocrine tumor. Primary PGs are rare to be in the thyroid gland, and most of them present slowly. Enlarging thyroid nodules over several years, and most of the time, it is a nonfunctional tumor. We are presenting a rare thyroid neoplasm diagnosis as primary thyroid PG. Due to rare presentation and occurrence, thyroid PGs are frequently mistaken for other common thyroid neoplasms. It is mandatory to increase awareness of its rare expression in the thyroid and its characteristic features to prevent diagnostic and therapeutic pitfalls.