Tachycardie ventriculaire récidivante révélant une sarcoïdose cardiaque

Alois Castro,Floriane Gilles,Sonia Marrakchi, Thibaut Wajchert, Philippe Rouvier,Fleur Cohen-Aubart, Géraldine Gibault-Genty,Jean-Louis Georges

Annales de Cardiologie et d'Angéiologie(2023)

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摘要
Sarcoidosis is an inflammatory disease whose diagnosis is suggested by clinical and paraclinical signs and confirmed by histological evidence showing granulomatosis without caseous necrosis. The clinical presentation is sometimes misleading and the diagnosis difficult to confirm. We report here the case of a young woman with cardiac sarcoidosis of difficult diagnosis, revealed by a myocardial infarction with normal coronary angiography and recurrent ventricular tachycardia. Multimodal imaging, combined with left ventricular endomyocardial biopsies guided by electrophysiological analysis and endocavitary mapping, finally confirmed the diagnosis, and allowed effective medical treatment.
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关键词
Sarcoïdose cardiaque,Tachycardie ventriculaire,Biopsie endomyocardique,IRM cardiaque,TEP-scan
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