The unmet needs for aortic diameter determination in patients with aortopathies

Detection and follow-up of a dilatation of the thoracic aorta with precise determination of the diameters are crucial to prevent dramatic consequences like aortic dissection in patients with hereditary aortopathies like Marfan syndrome (MFS), congenital heart disease and Turner syndrome [ 1 Yetman A.T. Graham T. The dilated aorta in patients with congenital cardiac defects. J. Am. Coll. Cardiol. 2009; 53: 461-467 Google Scholar , 2 Isselbacher E.M. Preventza O. Hamilton Black III, J. Augoustides J.G. Beck A.W. Bolen M.A. et al. 2022 ACC/AHA guideline for the diagnosis and Management of Aortic Disease: a report of the American Heart Association/American College of Cardiology Joint Committee on clinical practice guidelines. Circulation. 2022; 146: e334-e482 Google Scholar , 3 Detaint D. Faivre L. Collod-Beroud G. Child A.H. Loeys B.L. Binquet C. et al. Cardiovascular manifestations in men and women carrying a FBN1 mutation. Eur. Heart J. 2010; 31: 2223-2229 Google Scholar , 4 Thunstrom S. Thunstrom E. Naessen S. Berntorp K. Laczna Kitlinski M. Ekman B. et al. Aortic size predicts aortic dissection in turner syndrome - a 25-year prospective cohort study. Int. J. Cardiol. 2023; 373: 47-54 Google Scholar ]. Thoracic aorta diameters in Marfan patients: Intraindividual comparison of 3D modified relaxation-enhanced angiography without contrast and triggering (REACT) with transthoracic echocardiographyInternational Journal of CardiologyPreviewTo compare the measurement of aortic diameters using a novel flow-independent MR-Angiography (3D modified Relaxation-Enhanced Angiography without Contrast and Triggering (modified REACT)) and transthoracic echocardiography (TTE) in Marfan syndrome (MFS) patients. Full-Text PDF