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线粒体脑病引起的皮质聋1例及文献复习

Chinese Journal of Otology(2023)

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Abstract
由线粒体引起的听力损失大部分是感音神经性耳聋,出现皮质聋的极为罕见,国内目前没有报道.本例患者先前确诊线粒体脑病,此次以右手活动不便、口齿不清、听力丧失为主诉就诊.此患儿在确定为感音神经性耳聋及结合影像学听力学诊断后,确诊为中枢性传导通路的改变,即皮质聋.本文就线粒体脑病造成的皮质聋展开论述.
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