Anesthetic management in a patient with steinert syndrome undergoing laparoscopic cholecystectomy: A case report

A male patient, 47 years old, 67 kg, 1.70 m, with SS for 30 years, on preanesthetic evaluation to perform LC. He had muscular atrophy, myotonia, history of asthma and cataract, and had been submitted to tracheostomy and gastrostomy three years ago.Domperidone (20 mg), amitriptyline (25 mg), lactulone (13 g), muvinlax (14 g), dipyrone (500 mg), montelukast (10 mg), and loratadine (10 mg) were used. He had a brother and mother with SS.In electroneuromyography of the limbs, during mild exertion, he presented motor unit potentials of decreased durations and amplitudes in all muscles. During rest, fibrillation potentials and positive spikes wore observed.