Successful Mitral and Tricuspid Valve Repair for Dextrocardia With Situs Inversus Totalis

Dextrocardia with situs inversus is a rare congenital anomaly characterized by a right-sided heart apex and inversely rotated abdominal viscera. It is often autosomal recessive and involves 1 child in every 10,000 births. We report a case of dextrocardia with situs inversus totalis in a patient who underwent mitral valve repair through an extended transseptal approach for clinically relevant mitral regurgitation secondary to Barlow disease. The operation was successfully performed without complications, and the postoperative course was uneventful.