Absent Single Pulmonary Cusp Causing Isolated Pulmonary Valvar Regurgitation

Isolated congenital pulmonary valve regurgitation (IPVR) is very rare. Absent/ bicuspid/ dysplastic pulmonary valves are the common congenital causes of this condition. Here we present a rare cause of IPVR caused by absent single pulmonary cusp. A review of literature to establish timing and management of isolated pulmonary regurgitation is also attempted.