儿童吉兰-巴雷综合征谱系疾病伴急性全自主神经功能不全一例
Chinese Pediatric Emergency Medicine(2022)
Abstract
吉兰-巴雷综合征(Guillain-Barre syndrome,GBS)是以周围神经和神经根的脱髓鞘病变及小血管炎性细胞浸润为病理特点的自身免疫性周围神经病,是急性对称性弛缓性麻痹最常见的病因,可导致儿童死亡。急性自主神经功能紊乱是儿童GBS常见合并症,可导致心脏和血流动力学异常,如高血压、体位性低血压、心律失常、心力衰竭等并发症,严重影响预后。现通过1例GBS谱系疾病合并急性全自主神经功能不全(acute pandysautonomia,APD)病例回顾,提高对此病的认识。
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