A Case of Neurofibromatosis Type 2 in Whom the Tumor was Preserved During a Cochlear Implant Surgery

Neurofibromatosis type 2 (NF2) is a rare autosomal-dominant hereditary disease characterized by the presence of bilateral acoustic tumors. Some patients with NF2 suffer from bilateral profound hearing loss. An auditory brainstem implant (ABI) directly stimulating the cochlear nucleus is a traditional option for hearing rehabilitation in NF2 patients with profound hearing loss. Recently, cases of NF2 in whom hearing was successfully restored by cochlear implants (CIs) have been reported.