Urorectal septum malformation sequence with a giant calculus in the colon cyst in an adult

Introduction: The present article reports urinary and digestive system abnormalities, including retrocaval ureter, anal atresia, and colon duct cyst with duplicate urethra carrying a giant calculus in a 40-year-old man. Patient concerns: A 40-year-old man visited the hospital complaining of acute pain in the right lower abdomen. Diagnosis: Cystoscopy showed that the patient had duplicated urethra and bladder, and pathology showed that the duplicated bladder consisted of colon tissue, which led to the diagnosis of a urorectal septum malformation sequence. Interventions and outcomes: The calculus was removed, and the retrocaval ureter was treated with laparoscopic ureteroureterostomy. We followed up for 3 months after the secondary surgery, and there were no complications. Conclusion: A urorectal septum malformation sequence with a giant calculus in a colon cyst is rare. Hence, clinicians should be aware of the possibility of calculus formation in patients with a urorectal septum malformation sequence.