UNMASKING THE PREVALENCE OF AMYLOID CARDIOMYOPATHY IN THE REAL WORLD: RESULTS FROM PHASE 2 OF AC-TIVE STUDY, AN ITALIAN NATIONWIDE SURVEY Marco Merlo , Linda Pagura , Aldostefano Porcari , Matteo Cameli , Giuseppe Vergaro , Beatrice Musumeci , Elena Biagini , Marco Canepa , Lia Crotti , Massimo Imazio , Cinzia Forleo , Francesco Cappelli , Federico Perfetto , Stefano Favale , Gianluca Di Bella , Franca Dore , Francesca Girardi , Daniela Tomasoni , Rita Pavasini , Valeria Rella , Giuseppe Palmiero , Martina Caiazza , Maria Cristina Carella , Andrea Igoren Guaricci , Giovanna Branzi , Angelo Giuseppe Caponetti , Giulia Saturi , Giovanni La Malfa , Andrea Carlo Merlo , Alessandro Andreis , Francesco Bruno , Francesca Longo , Maddalena Rossi , Guerino Giuseppe Varrà , Riccardo Saro , Luca Di Ienno , Giuseppe De Carli , Elisa Giacomin , Chiara Arzilli , Giuseppe Limongelli , Camillo Autore , Iacopo Olivotto , Luigi Badano , Gianfranco Parati , Stefano Perlini , Marco Metra , Emdin Michele , Claudio Rapezzi , Gianfranco Sinagra EUROPEAN HEART JOURNAL SUPPLEMENTS(2022)
摘要
In a cohort of consecutive adults with echocardiographic findings suggestive of AC and preserved LVEF, the prevalence of AC (either ATTR or AL) was 29%. Easily available echocardiographic red flags, when combined together, demonstrated good diagnostic accuracy.
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关键词
amyloid cardiomyopathy, echocardiography, epidemiology, light chain amyloidosis, red flags, transthyretin amyloidosis
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