Wegener's Granulomatosis Vasculitis and Granuloma: A Case Report:

A 13-year-old girl was admitted to our hospital because of fatigue, oliguria, and edema of lower extremities. Her laboratory workup showed an acute renal failure (BUN= 225 mg/dl, Creatinine= 13.25 mg/dl). She also had a massive proteinuria. A renal biopsy showed cellular crescentic glomerulonephritis and positive C-ANCA. The serum Creatinine level decreased after treatment with high-dose methylprednisolone, rituximab and plasmapheresis. She did not require dialysis. This is a report of a rare case of GPA presenting with 100% cellular crescentic glomerulonephritis.