Neurenteric cyst of the craniocervical junction

✓ Neurenteric cysts of the craniocervical junction (CCJ) are very rare lesions. Their origin is the subject of long-standing controversy, but a failure during the embryogenic phase may be responsible for their formation. Accurate histopathological diagnosis may be difficult due to the similarity they share with other cystic lesions such as colloidal cysts, Rathke cysts, and cystic teratomas. Surgical removal is the treatment of choice for intracranial neurenteric cysts, but in some cases, infiltration of the surrounding structures may hinder complete resection. Three cases of neurenteric cysts located at the CCJ are reported.