以皮肤损害为首发表现的急性间歇性血卟啉病一例

Chinese Journal of Neuroimmunology and Neurology(2021)

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Abstract
1 病例报告 患者女,37 岁.因"皮肤红疹 1 年,反复抽搐 1 个月"于 2019-04-24 入院.1 年前无诱因出现面部及腹部散在红疹,面部红疹经太阳光照后出现少许水疱,腹部呈现少许斑片状,未就诊.1 个月前因情绪激动后出现心慌、气短、心前区疼痛、抽搐,头后仰,双眼及牙关紧闭,四肢伸直僵硬,伴全身抖动,尿失禁,无舌咬伤,约 20 min缓解,呼叫可应答,但反应迟钝.就诊于当地医院,诊治经过不详,病情略好转.
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