神经白塞病的诊治进展

Chinese Journal of Neuromedicine(2021)

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Abstract
白塞病(BD)是一种病因不明的慢性、反复发作性、多系统受累的血管炎性疾病,常见临床表现为复发性口腔和生殖器溃疡、葡萄膜炎和皮肤损害等。BD累及神经系统则称为神经白塞病(NBD),可表现为脑或脊髓实质损害、脑静脉血栓形成、脑动脉炎等。本文主要围绕NBD的临床表现、辅助检查、诊治等方面的研究进展进行综述,以期为NBD的临床诊疗提供参考。
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Key words
Beh?et's disease,Neuro-Beh?et's disease,Diagnosis,Therapy
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