Clinical features and outcomes of patients with myositis associated-interstitial lung disease.

Frontiers in medicine(2021)

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摘要
Specific ILD radiographic patterns such as NSIP and organizing pneumonia may herald underlying inflammatory myopathies. Hospitalized patients presenting with bilateral organizing pneumonia refractory to antibiotics should be meticulously evaluated for myositis associated-ILD even if there is no overt muscular involvement. Incorporation of ILD radiological patterns in the diagnostic criteria of inflammatory myopathies may lead to timely therapeutic interventions and positively impact patients' survival.
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关键词
amyopathic,interstitial lung disease,myositis,organizing pneumonia,survival
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