A Case of Congenital Syringocystadenoma Papilliferum

Syringocystadenoma papilliferum (SCAP) is a rare benign skin tumor that develops from the apocrine or eccrine glands. Here, we report the case of a 2-year-old girl who presented with an asymptomatic, slowly growing lesion on her scalp. On physical examination, a 2 cm × 1 cm red papillary plaque with a crusted surface was noted on her scalp. Histopathological examination revealed papillomatous expansion of the epidermis and cystic invaginations extending from the epidermis down to the deep dermis. The cystic structures were lined by papillae with two layers of columnar epithelium, which showed decapitation secretion. Based on the above clinicopathological findings, a diagnosis of congenital scalp SCAP was made.