Une cause rare de l’amylose AA : les épidermolyses bulleuses héréditaires
Néphrologie & Thérapeutique(2022)
摘要
Renal involvement is quite common in AA amyloidosis in patients with recessive dystrophic epidermolysis bullosa. Nephrotic syndrome and rapid decline in renal function renal are characteristic features. The prognosis is poor due to underlying conditions and the lack of an etiological treatment.
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关键词
Amylose AA,Épidermolyse bulleuse dystrophique récessive,Syndrome néphrotique
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