Pediatric Splenic Angiosarcoma

Angiosarcomas are malignant vascular neoplasms that usually occur in deep soft tissue. Patients diagnosed with angiosarcoma are usually elderly and are given poor prognoses. Pediatric splenic angiosarcoma is extremely rare, and its pathogenesis is not as well understood as that of older patients. We describe a case of 4-year-old male who had undergone splenectomy for splenic mass. Histopathological examination revealed primary splenic angiosarcoma. We then reviewed published literatures to characterize its clinical characteristics.