Youngest Reported Infant With Incomplete Cantrell Syndrome: Successful Correction Using Combined Repair

Pentalogy of Cantrell, also known as ectopia cordis, is a rare syndrome that involves intracardiac abnormalities and major defects in the diaphragm, abdominal wall, pericardium, and sternum. The survival rate of patients with complete pentalogy of Cantrell is as low as 20%. Survival is determined by the severity of cardiac anomalies, the type of surgery performed, and the timing of surgery. We present herein the youngest known infant with incomplete pentalogy of Cantrell successfully corrected using combined repair. The 23-day infant was treated by a team of pediatricians, cardiac surgeons, and plastic surgeons and achieved a satisfactory result without complications. He continued to thrive over a year of follow-up. It is crucial to choose the appropriate surgical treatment, proper timing of repair, and to encourage multidisciplinary treatment of patients with pentalogy of Cantrell.