Multiple cystic lesions of the jaws: Think about Gorlin–Goltz syndrome

Cystic lesions of the jaws are usually present as single lesions. Rarely, they can occur as multiple cysts occupying more than one quadrant of the jaws. It can be then part of a syndrome. Gorlin–Goltz syndrome is an autosomal dominant inherited condition comprising the principal triad of basal cell carcinomas, multiple jaw keratocysts, and skeletal anomalies. It is a syndrome of particular interest to the oral and maxillofacial health experts. Especially that the presence of jaw cysts is the early diagnostic feature of this syndrome, and this can be incidentally identified by routine dental radiographs. It is therefore important to know the main clinical and especially radiological features of this rare syndrome. The case presented is about a patient aged 24 who presented with multiple odontogenic keratocysts as the first signs of a Gorlin Goltz syndrome, that was later confirmed by other signs.