Desmoplastic Small Round Cell Tumor of the Kidney With Mainly Pulmonary Symptoms by 18F-FDG PET/CT.

Desmoplastic small round cell tumor (DSRCT) is a rare malignancy believed to originate from the serous membranes and it is highly aggressive with 5-year overall survival of 18.4%. Only a small number of DSRCT cases have been documented. Here, we report findings of DSRCT of the kidney on 18F-FDG PET/CT in a 30-year-old woman who presented with repetitive pulmonary infection and spontaneous pneumothorax.