婴儿肾外畸胎瘤样肾母细胞瘤1例

叶霞,沈和德,王莘媛, 徐万华,张德远

Chinese Journal of Clinical and Experimental Pathology(2020)

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Abstract
患儿男婴,4个月29天,因家长发现腹胀4个月余就诊.患儿无恶心呕吐、无排便排尿困难、无血便血尿.查体:腹部明显膨隆,触及一巨大质韧肿物,大小25cm ×20cm ×20cm,活动度差,边界尚清,腹部表面皮肤无红肿破溃、异常静脉曲张等.腹部CT示腹腔巨大占位性病变(图1).术中见肿瘤位于腹膜后,呈不规则球状,包膜完整,最大径25cm,压迫并与周围脏器及后腹膜严重粘连,双侧肾脏完整,顺肿瘤包膜完整切除肿瘤后送病理检查.
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