骨外黏液样软骨肉瘤2例临床病理学特征

Chinese Journal of Diagnostic Pathology(2014)

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Abstract
目的 探讨骨外黏液样软骨肉瘤(EMC)的临床病理学特征.方法 报道2例EMC的组织形态学和免疫组化特征,结合文献对其病理诊断和鉴别诊断进行分析.结果 2例EMS分别发生于左侧腹壁和右臀部.光镜下肿瘤呈多结节状,结节又分隔成大小不等的小叶,类圆形、梭形、星芒状肿瘤细胞包埋于黏液样基质中,肿瘤细胞具轻度异型性.免疫组化示vimentin和S-100为(+),Ki-67阳性率<2%.结论 EMC分为分化好的普通型和分化差的细胞型,两型均具有特异的组织学和细胞遗传学改变,免疫表型特异,Ki-67阳性率对预后有影响.
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Key words
Extraskeletal myxoid chondrosaroma,Clinicopathology,Differential diagnosis
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