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腮腺乳腺样分泌癌2例

Chinese Journal of Medical Imaging Technology(2020)

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Abstract
病例1,患儿男,11岁,左腮腺区肿物进行性增大1个月.查体:左腮腺区明显隆起,触及中等偏硬肿物,活动差,轻压痛.颈部CT示左腮腺浅叶约1.80 cm×1.70 cm类圆形均匀稍高密度结节,边缘清楚(图1A),考虑多形性腺瘤?行左腮腺肿物切除术,术中见左腮腺灰白或灰黄色形状不规则肿物,质软.病理:光镜下见微导管囊状扩张、囊内细胞增生呈筛状/乳头状,胞浆红染,未见病理性核分裂象(图1B);免疫组织化学:乳腺珠蛋白、表征肌上皮的CK5/6和波形蛋白阳性,肌酸激酶(CK/CK7)、S-100蛋白、E-钙黏附蛋白强阳性(+++).病理诊断:(左腮腺)乳腺样分泌性癌(mammary analogue secretory carcinoma,MASC).
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