左侧侧脑室血管瘤误诊1例

Chinese Journal of Medical Imaging Technology(2020)

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Abstract
患者男,14岁,无明显诱因头晕1年余,加重2天.查体:四肢肌力V级,肌张力正常,生理反射存在,病理反射未引出.MRI示左侧侧脑室内27 mm×33 mm×36 mm团块状长/短T1及长/短T2混杂信号(图1A、1B),于FLAIR序列图像呈混杂高低信号,DWI中少部分呈高信号;病变周边见短T2信号环绕,视交叉受压向下移位;增强扫描病灶内及周围片状强化(图1C);诊断:左侧侧脑室占位性病变伴出血.行左侧侧脑室占位切除术,术中见瘤体源自左侧侧脑室壁,穿过室间孔向三脑室生长,其中可见多个幼稚血管团,混合陈旧性出血,周围含铁血黄素沉着;沿含铁血黄素环切除肿瘤,其内可见粗大异常静脉结构.病理诊断:左侧侧脑室血管瘤,伴机化和钙化(图1D).
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