P-J综合征息肉恶变1例
CLINICAL FOCUS(1999)
Abstract
患者,男性,53岁.因反复腹泻伴下肢水肿8年余,加重7天,于1996年6月18日入院.患者自幼有口唇、手指黑斑,21岁时因"肠梗阻"、"肠套叠"2次手术治疗.8年前开始脐周隐痛,排糊状便,无脓血,无恶心呕吐,伴有下肢水肿.3年前肠镜检查:肛门至回盲部大片状息肉,以直肠、乙状结肠、降结肠为主.病理检验结果:全结肠及直肠管状腺瘤,有异形细胞生长.
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