Sturge-Weber综合征临床分析及影像诊断
Diagnostic Imaging & Interventional Radiology(2015)
Abstract
目的:探讨 Sturge-Weber 综合征的临床特点及 CT、MRI 表现及诊断。方法归纳8例 Sturge-Weber 综合征患者的临床表现、影像学特点,进行回顾性分析,并复习相关文献。结果8例均有脑内软脑膜血管瘤,其中3例伴有颜面部血管瘤,均位于三叉神经眼支分布区(均累及单侧);7例表现为癫痫发作,其中5例伴有头痛,1例伴有头晕及一侧肢体乏力;1例表现为单纯反复头痛;均无智力低下或青光眼。影像学检查可清晰显示脑萎缩、脑回样钙化、软脑膜广泛强化伴静脉畸形。结论 Sturge-Weber综合征是一种少见疾病,根据典型临床特点及CT、MRI等影像学检查有助于确诊。
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Key words
Sturge-Weber syndrome,Clinical features,Tomography,X-ray computed,Magnetic resonance imaging
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