伴多种酶异常升高的组织细胞坏死性淋巴结炎1例报告
Journal of Clinical Hepatology(2019)
Abstract
组织细胞坏死性淋巴结炎(histiocytic necrotizing lymphadenitis,HNL)由日本学者Kikuchi和Fujumoto于1972年首次报道,故又名菊池-藤本病(Kikuchi-Fujimoto's disease,KFD),也称菊池病(Kikuchi's disease),是一种良性、自限性疾病.HNL呈世界性分布,其中以亚洲地区和日本发病率较高.其特征性临床表现为区域性颈部淋巴结肿大伴压痛,常伴有发热和盗汗,较少见的症状包括体质量减轻、恶心、呕吐和咽痛,少数严重患者可出现多系统受累,明确诊断需依靠淋巴结活组织检查[1].
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