系统性红斑狼疮合并大疱表皮坏死松解型药疹伴药物超敏综合征1例

Rheumatism and Arthritis(2018)

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Abstract
系统性红斑狼疮(systemic lupus erythemato-sus,SLE)是一种原因未明的多系统、多器官损害的自身免疫性疾病,常累及皮肤、肌肉、关节、血液、神经等,临床上皮肤黏膜病变程度一般较轻,发生水疱、大疱及表皮剥脱者较少见.上海中医药大学附属龙华医院(简称本院)风湿科收治 1 例 SLE合并大疱表皮坏死松解型药疹伴药物超敏综合征并发弥散性血管内凝血的患者,经中西医结合疗法诊治痊愈,现报道如下.
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