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腹膜后中度恶性肌纤维母细胞肉瘤一例

Journal of Hepatopancreatobiliary Surgery(2020)

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Abstract
肌纤维母细胞肉瘤是一种罕见的恶性软组织肿瘤,主要发生在头颈部,其次是四肢,然后是躯干,很少累及腹膜后.经查阅,国内文献只报道了4例腹膜后恶性肌纤维母细胞肉瘤,3例为低度恶性[1],1例分级不明[2],国外报道1例高度恶性[3].通过本例报道,结合文献复习,讨论中度恶性腹膜后肌纤维母细胞肉瘤的诊断与治疗,增加临床医师对本病的认识.
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