婴儿脑内巨大海绵状血管瘤1例

Chinese Journal of Minimally Invasive Neurosurgery(2013)

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Abstract
1 病历摘要 女,6个月;以"突发抽搐10d,加重5d"入院.病儿是36周第1胎妊娠,自然顺产,出生体质量为2.20 kg.既往无外伤、癫痫样发作、局部神经功能障碍以及家族性血管畸形病史.查体:表情淡漠,无哭闹,听、视觉诱导反应迟钝,自主活动好.头颅无畸形,前囟无膨隆且张力不高.凝血常规无异常.MRI示:右侧顶叶约3.60 cm×4.11 cm×3.55 cm分叶状异常信号,T1WI、T2WI、压水压脂像呈高低混杂信号,病变周围见弧形短T1长T2异常信号,T2WI见明显黑环征.术中见病变位于脑表面,质地软,血运丰富,其周边有酱油色、已液化的血肿,并可见病变与脑组织间的暗黄色含铁血黄素层,行病变全切除.术后病理:右侧顶叶海绵状血管畸形(CM)伴陈旧性出血、血肿形成,灶状钙化、胶质细胞增生.术后病儿未见抽搐,术后10个月头部MRI示病灶无复发.
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