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新生儿先天性肺发育不良1例

Chinese Journal of Applied Clinical Pediatrics(2014)

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Abstract
先天性肺发育不良(congenital pulmonary hypoplasia,CPH)是胚胎发育障碍所致的先天性肺、支气管、肺血管畸形.CPH是一种罕见的肺发育异常疾病,全球发病率1/5 000 000[1],严重CPH病死率达71% ~95%.现将暨南大学附属第一医院收治的1例CPH报告如下. 1 临床资料 患儿,男,胎龄37+1周,因其母疤痕子宫剖宫产娩出,无窒息复苏史,出生体质量2 300 g,胎盘320 g,脐带细(直径<1 cm),羊水清,量少(350 mL),无胎膜早破,出生12 min以足月小样儿(匀称型)收入院.
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