原发性中枢神经系统淋巴瘤
JOURNAL OF CLINICAL NEUROLOGY(2003)
Abstract
原发性中枢神经系统淋巴瘤(PCNSL)是一类罕见的中枢神经系统肿瘤, 约占淋巴瘤的1%~2 %、脑肿瘤的1%~3%[1].随着器官移植、AIDS及各种先天免疫缺陷病的增加, 近年来发病率迅速上升[2].平均发病年龄在AIDS患者中为34岁,非AIDS患者为59岁 ;男女之比为1.5~3∶1[3].PCNSL原发于中枢神经系统,极少累及外周,临床表现变化多端,诊断困难,预后极差,需引起医务人员的重视.
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