儿童项部乳头状汗管囊腺瘤1例

Chinese Journal of Dermatovenerology of Integrated Traditional and Western Medicine(2019)

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Abstract
患儿女,6岁,项部皮色、淡红色皮疹4年余,伴有结痂.4年前发现项部正中皮色、淡黄色斑片,随年龄皮损渐长大增多,逐渐凸起于皮肤,呈串珠状排列的丘疹,中央略凹陷,伴渗出、角化及结痂,皮损长3cm,单个丘疹直径约3~4mm,无明显不适,曾给予激光及冷冻治疗,皮损仍复发.行皮肤活检术,皮肤病理示,见图1、2:部分表皮缺如伴外生性或内生性增生,皮肤浅中层内乳头状囊性增生物,囊内柱状上皮细胞乳头状增生,核椭圆形,胞浆红染嗜酸性,可见断头分泌现象,异型性不明显,核分裂少见,病理诊断为乳头状汗管囊腺瘤(Syringgocystadenoma papilliferum,SCAP).
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