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阿斯匹林治疗Still病诱发瑞氏综合征1例

MEDICAL JOURNAL OF NATIONAL DEFENDING FORCES IN NORTHWEST CHINA(2003)

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Abstract
患儿,女,7岁.因间断发热、皮疹4月余,加重半月入院.患儿无明显诱因出现发热,7 d后全身出现"红色皮疹",给予综合治疗后症状消失;半月之后再次出现高热,体温达40.0℃,伴寒战,无惊厥,呈弛张热型,给予"红霉素"等治疗,2周后发热症状消失;1周后再次高热,查血常规示:WBC 25×109*L-1,肝功2次均异常,B27(-),冷凝集试验、外斐氏、肥达氏反应、CRP、ASO、RF均正常,胸部X片正常,感染性骨髓象,给予抗感染等治疗,效果不佳,但是体温可自行恢复正常,数天后又升高;患病前期,每次高热前均有寒战,且伴有一过性皮疹.病程中,发现脾肿大,浅表淋巴结肿大,曾诊断"幼儿类风湿性关节炎",间断给予"阿斯匹林"退热.患儿发病期间,无盗汗、关节痛,精神食欲可,体重无明显减轻.
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