特发性肺间质纤维化影像学表现

刘红海, 申霞英,孟建华,张向民,刘岩

CHINESE JOURNAL OF MODERN DRUG APPLICATION(2013)

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Abstract
特发性肺间质纤维化(IPF),亦称隐源性纤维化肺泡炎或特发性间质性肺炎等,起病隐袭,大多数患者出现症状前病程超过6个月,好发于老年人,病变局限于肺,本病临床上多表现为刺激性干咳伴有进行性呼吸困难,常有杵状指(趾),组织病理学和(或)放射学表现具有普通型间质性肺炎(Usual Interstitial Pneumonia,UIP)特征.主要表现为弥漫性肺泡炎、肺泡单位结构紊乱和肺纤维化[1].
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