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Susac综合征的临床研究进展

Academic Journal of Second Military Medical University(2020)

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Abstract
Susac综合征(SS)目前认为是由免疫介导的以脑部、内耳和视网膜相关小血管的闭塞为主要表现的一种罕见病.SS以脑病、视网膜分支动脉闭塞和感觉神经性耳聋三联征为主要表现,但是由于临床症状相继出现,易导致漏诊、误诊.头颅MRI、荧光素眼底血管造影和听力检查有助于SS的早期诊断.SS的治疗较为复杂,需采用联合糖皮质激素、静脉注射Ig、免疫抑制治疗的综合治疗方案.
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