非活动性HBsAg携带者合并遗传性球形红细胞增多症1例并文献复习

Chinese Journal of Liver Diseases(Electronic Version)(2019)

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Abstract
慢性乙型肝炎免疫清除或活动引起的肝细胞或胆管细胞损伤表现为胆红素升高时,以直接胆红素升高为主.遗传性球形红细胞增多症(hereditary spherocytosis,HS)临床表现差异较大,需结合实验室检查、骨髓穿刺和基因检测等辅助诊断.慢性乙型肝炎患者出现以间接胆红素升高为主的肝功能损伤时,需警惕溶血、Gilbert综合征及Crigler-Najjar综合征等,目前尚无资料显示HS的发病与慢性乙型肝炎相关.本文现报道1例非活动性HBsAg携带者合并HS并进行文献复习.
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