脾切除术后发现漏诊甲型血友病一例

Chinese Journal of Hepatobiliary Surgery(2020)

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Abstract
患者男性,47岁,因“反复左下腹痛3d,脾切除术后1d”入湖南省人民医院治疗.查体:贫血貌,腹部稍膨隆,腹肌稍紧,全腹压痛,无反跳痛,移动性浊音阴性,听诊肠鸣音减弱.CT血管造影提示脾脏切除术后脾区出血.详细追问患者病史及完善相关检查后发现为轻型甲型血友病,予以输注去白悬浮红细胞、冷沉淀及凝血因子Ⅷ替代治疗后患者出血停止,腹腔内积血、积液逐步消失,住院13天后病情好转出院.
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