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暴发性1型糖尿病的临诊应对

Chinese Journal of Endocrinology and Metabolism(2014)

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Abstract
暴发性1型糖尿病(FT1D)是鉴别出来的一种特发性1型糖尿病的新亚型,主要临床表现为起病急骤,胰岛β细胞迅速破坏,出现高血糖症状1周内即发生糖尿病酮症或糖尿病酮症酸中毒,发病时血糖很高而HbA1C多接近正常,常伴血清胰酶水平升高.发病前多有类感冒样或胃肠道症状.本病具体发病机制尚未完全明确,可能在遗传背景基础上与病毒感染、自身免疫及妊娠等有关.本文报道2例FT1D,并对其临床特点、诊断、治疗等做一文献复习.
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Key words
Fulminant type 1 diabetes,Diagnosis,Treatment
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