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先天性心脏病相关肺动脉高压研究进展

Chinese Journal of Applied Clinical Pediatrics(2019)

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Abstract
肺动脉高压(PAH)是先天性心脏病(CHD)最常见的合并症,由于心脏解剖和病理生理学特点的复杂性和多样性以及多种适应性机制尚未被完全了解,先天性心脏病相关肺动脉高压( CHD-PAH)未能被足够重视.现归纳各国CHD-PAH的临床研究,总结CHD-PAH的疾病特点、转归及预后,提出目前尚未解决的问题和未来将迎来的挑战.
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Key words
Congenital heart disease,Pulmonary arterial hypertension,Child
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