Incidence, Treatment and Survival in Primary Central Nervous System Neuroblastoma.

-BACKGROUND: Primary central nervous system neuroblastoma (PCNSN) is a rare disease, and its inci-dence, treatment modalities, and survival remain poorly -nderstood. p p p -CONCLUSIONS: We updated epidemiologic informa-tion of PCNSN and showed that age, histologic type, tumor extension, and surgery were independent prognostic factors. Moreover, treatment modalities of these tumors are influenced by patient and tumor characteristics.