Occipito -cervical fusion in Cranio-Vertebral anomalies with basilar invagination

Basilar invagination are uncommon syndrome that occurs when the superior part of the odontoid (part of the C2 vertebrae) migrates upward through foramen magnum and that causes bulbomedullary compression. Basilar invagination are divided on bases of that causation in trau matic and other one is developmental. Mostly seen basilar invagination are developmental. Here with describe a case of 13yr old female with developmental craniovertebral junction abnormality in form of congenital atlanto axial dislocation with Platiebasia with basilar invagination which is treated with decompression and occipital plate and screw based posterior fixation with its clinical as well as radiological outcome. Keywords: Basilar invagination, AtlantoAxial dislocation, Platybasia, OC Fusion, Craniovertebral junction anomaly, Brainstem compression.