MR Imaging Features of Non Convulsive Status Epilepticus: A Great Masquerader

Variable clinical presentation and overlapping imaging findings make Non Convulsive Status Epilepticus (NCSE) a diagnostic challenge. NCSE is known to be a heterogeneous disorder with varied causes and several subtypes. Several disagreements exist as regards to its definition as well as the characteristic Electroencephalographic (EEG) features that are consistent with NCSE. We here present a case of nine-year-old female patient who presented with a recent onset history of regression of milestones since 5 to 6 months, and altered sensorium since 1-2 days. Contrast enhanced MRI brain was performed in this patient. This case highlights NCSE as a masquerader of inborn error of metabolism and attempts to address MR imaging findings of NCSE in acute intensive care setting.