吉兰-巴雷综合征谱系疾病的诊断

Chinese Journal of Applied Clinical Pediatrics(2016)

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Abstract
吉兰-巴雷综合征(GBS)临床特征为四肢弛缓性、对称性、上行性麻痹,伴颅神经和呼吸肌受累,脑脊液蛋白细胞分离及神经电生理改变.通常认为是累及周围神经系统的自身免疫性疾病.近些年来不断有GBS谱系疾病或GBS变异型的报道,血清抗体[如抗GQ1b抗体、抗神经节苷脂抗体]被发现.2014年由多国专家组成的GBS分类组制定并发表新的诊断和分类标准,旨在帮助神经科和非神经科医师在诊断GBS时,以一个简单易行且涵盖面广的诊断系统为依据.
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Key words
Guillain-Barré syndrome spectrum disorders,Guillain-Barré syndrome variant,Anti-GQ1b antibody,Anti-GM1 IgG antibody,Miller-Fisher syndrome
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