Phenylketonuric diet negatively impacts on butyrate production.
Nutrition, Metabolism and Cardiovascular Diseases(2018)
摘要
•Despite progress in treatment, PKU cornerstone of management is made by diet.•Diet is one of the most relevant factors influencing gut Microbiota composition.•Microbial richness, hallmark of gut dysbiosis, was reduced in PKU children.
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关键词
Phenylketonuria,Short chain fatty acids,Butyrate,Faecalibacterium prausnitzii
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