The Subclinical Cardiomyopathy of Friedreich's Ataxia in a Pediatric Population.

•Subclinical hypertrophic cardiomyopathy occurs commonly in early stages of Friedreich's ataxia.•Left ventricular mass is associated with depression of systolic and diastolic function.•Concentric remodeling and hypertrophy are 2 forms of ventricular remodeling.•Concentric hypertrophy is associated with depressed ventricular function.