Einseitige auditorische Neuropathie : Eine seltene Differenzialdiagnose einer einseitigen Resthörigkeit

Auditory neuropathy presents with normal otoacoustic emissions combined with pathological findings in brainstem evoked response audiometry (BERA). Normally, the auditory neuropathy is bilateral. We report about a 9 year old child where we could diagnose a unilateral deafness in spite of regularTEOAE and DPOAE. BERA showed no reproducible biosignals when the right ear was stimulated with alternating click stimuli at a level of 80 dB. On the left side, the latency of the potentials was normal. A cranial MRI showed normal anatomy. In order to determine a unilateral deafness, objective tests (e.g., OAE, BERA) and subjective tests should be used.