A Case of Sagittal Splitting Ramus Osteotomy in Osteogenesis Imperfecta with Mandibular Prognathism

Osteogenesis imperfecta is a hereditary bone disorder with friable bone and is caused by gene mutation of type 1 collagen. Clinical features are multiple fractures, bone deformity, blue sclera, dentinogenesis and so on. Complications are abnormal fracture, bleeding tendency, and malignant hyperthermia. These problems make surgery difficult.This case report describes osteogenesis imperfecta with a mandibular prognathic patient who had marked changes in the occlusion and profile after sagittal splitting ramus osteotomy.